Congenital cholesteatoma of the mastoid process: cases of diagnosis and surgical treatment

Zelenkova V.N.

Research Clinical Institute of Otorinolaryngology named after. L.I. Sverzhevsky

Zelenkov A.V.

Research Clinical Institute of Otorinolaryngology named after. L.I. Sverzhevsky

Kryukov A.I.

Sverzhevsky Research Clinical Institute of Otorhinolaryngology;
Pirogov Russian National Research Medical University

ORCID: 0000-0002-0149-0676

Stepanova E.A.

M.F. Vladimirsky Moscow Regional Clinical Research Institute

ORCID: 0000-0002-9037-0034

Moseykina L.A.

Sverzhevsky Research Clinical Institute of Otorhinolaryngology

Congenital cholesteatoma of the mastoid process: cases of diagnosis and surgical treatment

Authors:

Zelenkova V.N., Zelenkov A.V., Kryukov A.I., Stepanova E.A., Moseykina L.A.

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Journal: Russian Bulletin of Otorhinolaryngology. 2022;87(4): 95‑101

DOI: 10.17116/otorino20228704195

Downloaded: 83

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To cite this article:

Zelenkova VN, Zelenkov AV, Kryukov AI, Stepanova EA, Moseykina LA. Congenital cholesteatoma of the mastoid process: cases of diagnosis and surgical treatment. Russian Bulletin of Otorhinolaryngology. 2022;87(4):95‑101. (In Russ.)
https://doi.org/10.17116/otorino20228704195

Подписка 2025 (Russian Bulletin of Otorhinolaryngology)

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A brief review of the epidemiology and pathogenesis of congenital cholesteatoma (CC) of the temporal bone pyramid is presented, classifications reflecting the degree of spread or localization of the process are considered. Variants of local CCs of the mastoid process don’t fit into these classifications, as well as there is no statistics on the frequency of their detection and treatment due to the rarity of this pathology. Clinical cases of diagnosis, surgical treatment of CC of the mastoid process and its results are described. Clinical examples indicate a long-term asymptomatic course of CC of the mastoid process, accompanied by a pronounced destructive process in the mastoid process. Early surgical treatment makes it possible to remove the neoplasm as radically as possible and preserve hearing function.

Keywords:

congenital cholesteatoma of the mastoid process

subperiosteal abscess

surgical treatment

Authors:

Zelenkova V.N.

Research Clinical Institute of Otorinolaryngology named after. L.I. Sverzhevsky

Zelenkov A.V.

Research Clinical Institute of Otorinolaryngology named after. L.I. Sverzhevsky

Kryukov A.I.

Sverzhevsky Research Clinical Institute of Otorhinolaryngology;
Pirogov Russian National Research Medical University

ORCID: 0000-0002-0149-0676

Stepanova E.A.

M.F. Vladimirsky Moscow Regional Clinical Research Institute

ORCID: 0000-0002-9037-0034

Moseykina L.A.

Sverzhevsky Research Clinical Institute of Otorhinolaryngology

Received:

07.05.2020

Accepted:

25.05.2020

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