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Ponomarev A.E.

Central Research Institute of Dentistry and Maxillofacial Surgery

Butsan S.B.

Central Research Institute of Dentistry and Maxillofacial Surgery

Iigitaliev Sh.N.

Central Research Institute of Dentistry and Maxillofacial Surgery

Lafishev A.I.

Central Research Institute of Dentistry and Maxillofacial Surgery

Bulat S.G.

Central Research Institute of Dentistry and Maxillofacial Surgery

Seleznev V.A.

Central Research Institute of Dentistry and Maxillofacial Surgery

Comprehensive rehabilitation of patients with anhydrotic (hypohydrotic) ectodermal dysplasia: clinical case

Authors:

Ponomarev A.E., Butsan S.B., Iigitaliev Sh.N., Lafishev A.I., Bulat S.G., Seleznev V.A.

More about the authors

Journal: Stomatology. 2025;104(5): 64‑72

DOI: 10.17116/stomat202510405164

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Table of contents

COMPREHENSIVE REHABILITATION OF PATIENTS WITH ANHYDROTIC (HYPOHYDROTIC) ECTODERMAL DYSPLASIA: CLINICAL CASE
COMPREHENSIVE REHABILITATION OF PATIENTS WITH ANHYDROTIC (HYPOHYDROTIC) ECTODERMAL DYSPLASIA: CLINICAL CASE

To cite this article:

Ponomarev AE, Butsan SB, Iigitaliev ShN, Lafishev AI, Bulat SG, Seleznev VA. Comprehensive rehabilitation of patients with anhydrotic (hypohydrotic) ectodermal dysplasia: clinical case. Stomatology. 2025;104(5):64‑72. (In Russ.)
https://doi.org/10.17116/stomat202510405164

Подписка 2026 Стоматология (Stomatology)
МСФ на ЯМ
Использование инфографики авторами научных работ
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Abstract:

Ectodermal dysplasia (ED) is a group of rare hereditary disorders characterized by impaired development of ectodermal derivatives. The anhidrotic (hypohidrotic) form of ED is accompanied by pronounced hypoplasia of the jaws, partial or complete adontia, leading to functional impairments (difficulty chewing, swallowing, and speaking) and pronounced aesthetic changes. These factors have a significant impact on the quality of life of patients, causing psychological discomfort and social maladjustment. The article presents in detail a clinical case of a 20-year-old patient with anhidrotic (hypohidrotic) ED, who underwent comprehensive surgical rehabilitation.

Keywords:

ectodermal dysplasia
anhydrotic (hypohydrotic) ectodermal dysplasia
jaw bone grafting
dental implantation

Authors:

Ponomarev A.E.

Central Research Institute of Dentistry and Maxillofacial Surgery

Butsan S.B.

Central Research Institute of Dentistry and Maxillofacial Surgery

Iigitaliev Sh.N.

Central Research Institute of Dentistry and Maxillofacial Surgery

Lafishev A.I.

Central Research Institute of Dentistry and Maxillofacial Surgery

Bulat S.G.

Central Research Institute of Dentistry and Maxillofacial Surgery

Seleznev V.A.

Central Research Institute of Dentistry and Maxillofacial Surgery

Received:

07.12.2024

Accepted:

28.03.2025

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References:

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