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Blagova O.V.

GBOU VPO Pervyĭ MGMU im. I.M. Sechenova

Nedostup A.V.

GBOU VPO Pervyĭ MGMU im. I.M. Sechenova

Shumakov D.V.

FNTs transplantologii i iskusstvennykh organov im. akad. V.I. Shumakova, Moskva

Poptsov V.N.

Federal'nyĭ nauchnyĭ tsentr transplantologii i iskusstvennykh organov im. akademika V.I. Shumakova Minzdravsotsrazvitiia RF

Kormer A.Ia.

FGBU "Federal'nyĭ nauchnyĭ tsentr transplantologii i iskusstvennykh organov im. akad. V.I. Shumakova" Minzdrava Rossii, Moskva

Saitgareev R.Sh.

FNTs transplantologii i iskusstvennykh organov im. akad. V.I. Shumakova, Moskva

Zakharevich V.M.

FNTs transplantologii i iskusstvennykh organov im. akad. V.I. Shumakova, Moskva

Sergushkina N.G.

GBOU VPO Pervyĭ MGMU im. I.M. Sechenova

Shestak A.G.

FGBU "Rossiĭskiĭ nauchnyĭ tsentr khirurgii im. akad. B.V. Petrovskogo" RAMN, Moskva

Zakliaz'minskaia E.V.

FGBU RNTsKh im. akad. B.V. Petrovskogo RAMN

Filatov A.G.

FGBU "Nauchnyĭ tsentr serdechno-sosudistoĭ khirurgii im. A.N. Bakuleva" RAMN, Moskva

Mozheĭko N.P.

FGBU "Federal'nyĭ nauchnyĭ tsentr transplantologii i iskusstvennykh organov im. akad. V.I. Shumakova" Minzdrava Rossii, Moskva

Successful treatment of progressive cardiomyopathy in myodystrophy Emery-Dreifuss: from radiofrequency ablation and implantation of cardioverter to urgent heart transplantation

Authors:

Blagova O.V., Nedostup A.V., Shumakov D.V., Poptsov V.N., Kormer A.Ia., Saitgareev R.Sh., Zakharevich V.M., Sergushkina N.G., Shestak A.G., Zakliaz'minskaia E.V., Filatov A.G., Mozheĭko N.P.

More about the authors

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To cite this article:

Blagova OV, Nedostup AV, Shumakov DV, et al. . Successful treatment of progressive cardiomyopathy in myodystrophy Emery-Dreifuss: from radiofrequency ablation and implantation of cardioverter to urgent heart transplantation. Russian Journal of Cardiology and Cardiovascular Surgery. 2014;7(6):96‑102. (In Russ.)

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References:

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  2. Blagova O.V., Nedostup A.V., Sedov V.P. i dr. Rezul'taty implantacii resinkhroniziruiushchikh ustroĭstv i kardioverterov-defibrilliatorov u bol'nykh s DKMP. Vserossiĭskiĭ s''ezd aritmologov,5-ĭ: Materialy. Annaly aritmol 2013; 2: 160 (prilozhenie).
  3. Klinicheskie rekomendacii VNOA po provedeniiu élektrofiziologicheskikh issledovaniĭ, kateternoĭ abliacii i primeneniiu implantiruemykh antiaritmicheskikh ustroĭstv. M: MAKSPRESS 2013.
  4. Rudenskaia G.E., Tverskaia S.M., Chukhrova A.L. i dr. Kliniko-genealogicheskoe i molekuliarno-geneticheskoe issledovanie myshechnoĭ distrofii émeri-Dreĭfusa. Zhurn nevrol i psikhiatr 2006; 106: 10: 58-85.
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  8. Caforio A.L., Mahon N.G., Baig M.K. et al. Prospective familial assessment in dilated cardiomyopathy: cardiac autoantibodies predict disease development in asymptomatic relatives. Circulation 2007; 115: 1: 76-83.
  9. Carvalho A.A., Levy J.A., Gutierrez P.S. et al. Emery-Dreifuss muscular dystrophy: anatomical-clinical correlation (case report). Arq Neuropsiquiatr 2000; 58: 4: 1123-1127.
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  11. Finsterer J., Stöllberger C., Steger C., Gatterer E. Catheter ablation of multiple accessory pathways in duchenne muscular dystrophy. Korean Circ J 2013; 43: 2: 115-118.
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  21. van Spaendonck-Zwarts K.Y., van Rijsingen I.A., van den Berg M.P. et al. Genetic analysis in 418 index patients with idiopathic dilated cardiomyopathy: overview of 10 years' experience. Eur J Heart Fail 2013; 15: 6: 628-636.
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