Clinical manifestations of the onset and diagnostic problems in children with moyamoya disease

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Moyamoya disease in children is a rarely diagnosed entity. Frequent headache is the first symptom of the disease. Headache associated with moya-moya disease (HAMD) is a separated entity reported in the literature. Variants of onset, a spectrum of primary diagnoses and diagnosis verification rate of moyamoya disease in 7 children are presented. A clinical case of moya-moya disease in a 9-year boy, who was primarily diagnosed with migraine with aura, is reported. The results presented by the authors as well as literature data indicate the necessity of using magnetic-resonance angiography in children with headache attacks and focal neurologic symptoms to identify this progressive vascular pathology and timely recommend a surgical treatment.

Keywords:

moyamoya disease

headache

children age

Authors:

L'vova O.A.

Kafedra nevrologii detskogo vozrasta i neonatologii

Jevneronok I.V.

Belarusian Medical Academy of Postgraduate Education, Minsk, Belarus

Shalkevich L.V.

Belarusian Medical Academy of Postgraduate Education, Minsk, Belarus

Prusakova T.S.

Mogilev Regional Children Hospital, Mogilev, Belarus

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