Oral manifestations of KID syndrome: rare clinical case

Korolenkova M.V.; Dmitrieva N.A.; Babichenko I.I.; Gusova Yu.V.; Poberezhnaya A.A.

doi:https://doi.org/10.17116/stomat20199804193

Korolenkova M.V.

Central Research Institute of Dentistry and Maxillofacial Surgery, Moscow

Dmitrieva N.A.

Babichenko I.I.

Russian University of People’s Friendship, Moscow, Russia, 117198

Gusova Yu.V.

Central Research Institute of Dentistry and Maxillofacial Surgery, Moscow, Russia

Poberezhnaya A.A.

Central Research Institute of Dentistry and Maxillofacial Surgery, Moscow, Russia

Oral manifestations of KID syndrome: rare clinical case

Authors:

Korolenkova M.V., Dmitrieva N.A., Babichenko I.I., Gusova Yu.V., Poberezhnaya A.A.

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Journal: Stomatology. 2019;98(4): 93‑95

DOI: 10.17116/stomat20199804193

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To cite this article:

Korolenkova MV, Dmitrieva NA, Babichenko II, Gusova YuV, Poberezhnaya AA. Oral manifestations of KID syndrome: rare clinical case. Stomatology. 2019;98(4):93‑95. (In Russ.)
https://doi.org/10.17116/stomat20199804193

Подписка 2026 Стоматология (Stomatology)

Использование инфографики авторами научных работ

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Abstract:

The paper presents a rare clinical case of an infant with KID (Keratitis, Ichthyosis, Deafness) syndrome (about 100 patients reported so far) admitted for histological verification of oral mucosa lesions. Disease pathogenesis defines inadequate reparation and skin and mucosa innate immunity defect leading to higher incidence of bacterial and fungal infections, so the 4-years old girl received treatment for vegetating candidiasis of the oral mucosa for several weeks with no clinical improvement. Initial examination showed that the oral lesions resulted from sharp edges of severely affected carious teeth. Histological study of multifocal biopsy revealed pyogenic granulomas and no signs of SCC. Teeth extraction and symptomatic treatment leaded to significant clinical improvement and some remained mucosal changes may be attributed to syndrome manifestations.

Keywords:

KID syndrome

oral mucosa

oral microbiota

histological study

Authors:

Korolenkova M.V.

Central Research Institute of Dentistry and Maxillofacial Surgery, Moscow

Dmitrieva N.A.

Babichenko I.I.

Russian University of People’s Friendship, Moscow, Russia, 117198

Gusova Yu.V.

Central Research Institute of Dentistry and Maxillofacial Surgery, Moscow, Russia

Poberezhnaya A.A.

Central Research Institute of Dentistry and Maxillofacial Surgery, Moscow, Russia

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References:

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