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Smirnova I.O.

Sankt-Peterburgskiĭ gosudarstvennyĭ universitet, Sankt-Peterburg, Rossiia, 199106

Petunova Ia.G.

Sankt-Peterburgskiĭ gosudarstvennyĭ universitet, Sankt-Peterburg, Rossiia, 199106

Belousova I.E.

Military Medical Academy named after S.M. Kirov, RF Defence Ministry, St. Petersburg, Russia, 194044

Konstantinova A.M.

Federal State Budgetary Educational Institution of Higher Professional Education «St. Petersburg State University», St. Petersburg, Russia;
The State Budgetary Healthcare Institution «Clinical research and practical center for specialized oncological care», St. Petersburg, Russia;
Private educational institution of higher education «Saint-Petersburg Medico-Social Institute», St. Petersburg, Russia

Shelekhova K.V.

The State Budgetary Healthcare Institution «Clinical research and practical center for specialized oncological care», St. Petersburg, Russia;
Private educational institution of higher education «Saint-Petersburg Medico-Social Institute», St. Petersburg, Russia

Oganesyan M.V.

Chair of Normal Anatomy, Sechenov First Moscow State Medical University of Ministry of Health of Russia, Moscow, Russia

Difficulties of the diagnosis of the extramammary Paget disease

Authors:

Smirnova I.O., Petunova Ia.G., Belousova I.E., Konstantinova A.M., Shelekhova K.V., Oganesyan M.V.

More about the authors

Journal: Russian Journal of Clinical Dermatology and Venereology. 2018;17(3): 36‑41

DOI: 10.17116/klinderma201817342

Read: 2991 times

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Table of contents

DIFFICULTIES OF THE DIAGNOSIS OF THE EXTRAMAMMARY PAGET DISEASE
DIFFICULTIES OF THE DIAGNOSIS OF THE EXTRAMAMMARY PAGET DISEASE

To cite this article:

Smirnova IO, Petunova IaG, Belousova IE, Konstantinova AM, Shelekhova KV, Oganesyan MV. Difficulties of the diagnosis of the extramammary Paget disease. Russian Journal of Clinical Dermatology and Venereology. 2018;17(3):36‑41. (In Russ.)
https://doi.org/10.17116/klinderma201817342

Подписка 2026 Клиническая дерматология и венерология (Russian Journal of Clinical Dermatology and Venereology)
МСФ на ЯМ
Использование инфографики авторами научных работ
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Abstract:

Extramammary Paget disease (EMPD) is a rare tumor, which typically involve genitalia. The lesions are often similar to chronic dermatoses, which complicates the diagnosis of the disease. Skin biopsy with histological and immunohistochemical examination is required to verify the diagnosis of EMPD. In most cases, surgical resection accompanied by follow-up is used, but the relapse rate is still quite high. The paper focuses on the pathogenesis, diagnosis and treatment of EMPD and reports a case of a female patient with EMPD, who was diagnosed 5 years after the onset of the disease.

Keywords:

extramammary Paget’s disease
vulva
clinical presentation
dermoscopy
pathomorphology
treatment

Authors:

Smirnova I.O.

Sankt-Peterburgskiĭ gosudarstvennyĭ universitet, Sankt-Peterburg, Rossiia, 199106

Petunova Ia.G.

Sankt-Peterburgskiĭ gosudarstvennyĭ universitet, Sankt-Peterburg, Rossiia, 199106

Belousova I.E.

Military Medical Academy named after S.M. Kirov, RF Defence Ministry, St. Petersburg, Russia, 194044

Konstantinova A.M.

Federal State Budgetary Educational Institution of Higher Professional Education «St. Petersburg State University», St. Petersburg, Russia;
The State Budgetary Healthcare Institution «Clinical research and practical center for specialized oncological care», St. Petersburg, Russia;
Private educational institution of higher education «Saint-Petersburg Medico-Social Institute», St. Petersburg, Russia

Shelekhova K.V.

The State Budgetary Healthcare Institution «Clinical research and practical center for specialized oncological care», St. Petersburg, Russia;
Private educational institution of higher education «Saint-Petersburg Medico-Social Institute», St. Petersburg, Russia

Oganesyan M.V.

Chair of Normal Anatomy, Sechenov First Moscow State Medical University of Ministry of Health of Russia, Moscow, Russia

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References:

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