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Shchederkina I.O.

Livshtz M.I.

Morozov Moscow children clinical hospital, Pediatric stroke center, Moscow, Russia;
Pirogov Russian National Research Medical University, Moscow, Russia

Kuzmina E.V.

Morozov Moscow children clinical hospital, Pediatric stroke center, Moscow, Russia

Seliverstova E.V.

Morozov Moscow children clinical hospital, Pediatric stroke center, Moscow, Russia

Kessel A.E.

Morozov Moscow children clinical hospital, Pediatric stroke center, Moscow, Russia

Petriaĭkina E.E.

Morozovskaia detskaia gorodskaia klinicheskaia bol'nitsa

Sturge—Weber syndrome in children. Clinical features, diagnosis and approaches to therapy on the example of three clinical cases

Authors:

Shchederkina I.O., Livshtz M.I., Kuzmina E.V., Seliverstova E.V., Kessel A.E., Petriaĭkina E.E.

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Journal: S.S. Korsakov Journal of Neurology and Psychiatry. 2019;119(11‑2): 55‑64

DOI: 10.17116/jnevro201911911255

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To cite this article:

Shchederkina IO, Livshtz MI, Kuzmina EV, Seliverstova EV, Kessel AE, Petriaĭkina EE. Sturge—Weber syndrome in children. Clinical features, diagnosis and approaches to therapy on the example of three clinical cases. S.S. Korsakov Journal of Neurology and Psychiatry. 2019;119(11‑2):55‑64. (In Russ.)
https://doi.org/10.17116/jnevro201911911255

 
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Sturge—Weber syndrome belongs to the group of phacomotoses and is characterized by a combined lesion of the skin, eyes, nervous system and internal organs. The clinical course of Sturge—Weber syndrome is quite diverse. Of particular interest in the practice of pediatric neurology and neurosurgery is the fact that 72—90% of patients present with epilepsy. Of particular difficulty is the differential diagnosis of epileptic seizures and stroke-like episodes. The article presents clinical cases of patients with Sturge—Weber syndrome of various ages with epileptic seizures and transient ischemic attacks.

Keywords:

Sturge—Weber syndrome
epilepsy
stroke-like episodes

Authors:

Shchederkina I.O.

Livshtz M.I.

Morozov Moscow children clinical hospital, Pediatric stroke center, Moscow, Russia;
Pirogov Russian National Research Medical University, Moscow, Russia

Kuzmina E.V.

Morozov Moscow children clinical hospital, Pediatric stroke center, Moscow, Russia

Seliverstova E.V.

Morozov Moscow children clinical hospital, Pediatric stroke center, Moscow, Russia

Kessel A.E.

Morozov Moscow children clinical hospital, Pediatric stroke center, Moscow, Russia

Petriaĭkina E.E.

Morozovskaia detskaia gorodskaia klinicheskaia bol'nitsa

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