Disseminated ependymal dysembryoplastic neuroepithelial tumor: a case report and literature review

Kushel YuV, Kutin MA, Ivanov VV, et al. . Disseminated ependymal dysembryoplastic neuroepithelial tumor: a case report and literature review. Burdenko's Journal of Neurosurgery. 2024;88(4):92‑99. (In Russ., In Engl.)
https://doi.org/10.17116/neiro20248804192

Подписка 2025 Журнал «Вопросы нейрохирургии» имени Н.Н. Бурденко (Burdenko's Journal of Neurosurgery)

Использование инфографики авторами научных работ

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MATERIAL AND METHODS

We present a rare case of T1- and T2-negative ventricular system tumor. Only FIESTA imaging revealed dissemination with multiple focal lesions of the third ventricle, its bottom and lateral walls, anterior horns of lateral ventricles, cerebellar vermis, cervical and lumbar spinal cord.

RESULTS

The patient underwent transcortical endoscopic biopsy of the third ventricle tumor with simultaneous ventriculoperitoneal shunting. DNET was diagnosed, and radiotherapy was subsequently performed. Literature data on this issue were analyzed.

CONCLUSION

To date, disseminated forms of DNET are extremely rare. X-ray features and morphological results allow us to establish the correct diagnosis and determine further treatment strategy.

Keywords:

dysembryoplastic neuroepithelial tumor

third ventricle

endoscopic transcortical access

neurosurgery

Authors:

Kushel Yu.V.

Burdenko Neurosurgical Center;
Central Clinical Hospital with Polyclinic of the Presidential Administration

ORCID: 0000-0001-7136-0693

Kutin M.A.

Burdenko Neurosurgical Center

ORCID: 0000-0002-6520-4296

Ivanov V.V.

Burdenko Neurosurgical Center

ORCID: 0000-0003-3827-8676

Chernov I.V.

Burdenko Neurosurgical Center

ORCID: 0000-0002-9789-3452

Adueva D.Sh.

Burdenko Neurosurgical Center

ORCID: 0009-0003-1915-8107

Pronin I.N.

Burdenko Neurosurgical Center;
Russian Medical Academy of Continuing Professional Education

SPIN RSCI: 9223-9217
Scopus AuthorID: 7006011755
ORCID: 0000-0002-4480-0275

Shishkina L.V.

Burdenko Neurosurgical Center

ORCID: 0000-0003-0147-2301

Konovalova E.S.

Burdenko Neurosurgical Center

ORCID: 0000-0002-3523-9885

Kalinin P.L.

Burdenko Neurosurgical Center

ORCID: 0000-0001-9333-9473

Received:

30.01.2024

Accepted:

31.05.2024

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