Aim — to compare the results of surgical correction of discrete subaortic stenoses depending on the use of additional myectomy. Material and methods. We have analyzed data of 163 patients aged 3 months — 18 years with discrete subaortic stenoses who were operated for the period January 2003 to December 2013. The research is multicenter. The main material was taken at Novosibirsk Research Institute of Circulation Pathology. 67 patients were divided into two groups after application of inclusion and exclusion criteria. The 1st group had 35 children after isolated repair of discrete subaortic stenoses; the 2nd included 32 patients who underwent valvular repair and septal myectomy. Primary endpoints were development of restenoses and reoperation for subaortic restenosis. Results. In postoperative period peak pressure gradient was significantly lower in group of additional myectomy (p=0.04). However there were no differences in mean pressure gradient (p=0.17), incidence of atrioventricular blockage (p=0.6) between both groups. Peak and mean pressure gradients were also similar in 1 and 2 years after surgery (p=0.9 and p=0.59 respectively in 1 year; p=0.58 and p=0.79 respectively in 2 year). Septal myectomy does not change significantly time to restenosis according to log-rank value (р=0.16). The median and interquartile range of follow-up period were 40 (26; 86) months in the 1st group and 25 (23.5; 41.5) months in the 2nd group. Conclusion. Septal myectomy for discrete subaortic stenoses doesn’t increase the incidence of AV-block. There is significant decrease of peak pressure gradient postoperatively. However, the method doesn’t influence mid-term incidence of restenosis and reoperation.