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Sectoral schwannomatosis of the lower extremities

Sectoral schwannomatosis of the lower extremities

Authors:
Ангелина Викторовна Городнина,
Дарья Александровна Ситовская,
Андрей Юрьевич Орлов

Журнал: Вопросы нейрохирургии имени Н.Н. Бурденко. 2026;90(3):43-48.

DOI: 10.17116/neiro20269003143

Read: 1116 раз

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Abstract

INTRODUCTION

Sectoral schwannomatosis is a rare disease with damage to one nerve of the limb by multiple tumors without pathological foci in other anatomical areas. Surgery is the optimal treatment for segmental schwannomatosis and progression of clinical manifestations.

OBJECTIVE

To present our own experience in surgical treatment of patients with segmental schwannomatosis of the sciatic nerve and its branches over the past 5 years.

MATERIAL AND METHODS

The authors present 3 patients with sectoral schwannomatosis of the sciatic nerve who underwent surgical treatment. All patients underwent total nerve-sparing resection of tumors.

CONCLUSION

Management of sectoral schwannomatosis is individual, although surgical treatment involving total nerve-sparing tumor resection is preferable. Further data collection is necessary for a more detailed analysis of segmental schwannomatosis.

Keywords

  • schwannomatosis
  • sciatic nerve
  • sectoral schwannomatosis
  • segmental schwannomatosis
  • peripheral nerve tumor
  • schwannoma

Дата поступления: 08.07.2025

Дата принятия в печать: 12.03.2026

Дата публикации: 25.05.2026

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