Ocular involvement in Parry—Romberg syndrome

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Parry-Romberg syndrome (PRS) is a rare degenerative disease of unknown etiology, characterized by slow progressive hemifacial atrophy of the soft tissues (subcutaneous fat, muscles), cartilage and bones. Beside hemifacial atrophy, various ophthalmic and periocular manifestations of PRS has been described. Progressive enophthalmos and eyelid changes are only some of many other symptoms, as the disease can affect all layers of the eyeball. This article reviews literature on ophthalmic manifestations of PRS and reports our own case and treatment approach for a patient with this pathology.

Keywords:

hemifacial atrophy

Parry—Romberg syndrome

enophthalmos

lagophthalmos

Authors:

Sheptulin V.A.

Krasnov Research Institute of Eye Diseases

ORCID: 0000-0002-5709-4795

Grusha Ya.O.

Krasnov Research Institute of Eye Diseases;
I.M. Sechenov First Moscow State Medical University (Sechenov University)

ORCID: 0000-0002-6461-8243

Received:

17.01.2023

Accepted:

04.10.2023

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