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Sheptulin V.A.

Krasnov Research Institute of Eye Diseases

Grusha Ya.O.

Krasnov Research Institute of Eye Diseases;
I.M. Sechenov First Moscow State Medical University (Sechenov University)

Ocular involvement in Parry—Romberg syndrome

Authors:

Sheptulin V.A., Grusha Ya.O.

More about the authors

Journal: Russian Annals of Ophthalmology. 2023;139(6): 144‑150

DOI: 10.17116/oftalma2023139061144

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Table of contents

OCULAR INVOLVEMENT IN PARRY—ROMBERG SYNDROME
OCULAR INVOLVEMENT IN PARRY—ROMBERG SYNDROME

To cite this article:

Sheptulin VA, Grusha YaO. Ocular involvement in Parry—Romberg syndrome. Russian Annals of Ophthalmology. 2023;139(6):144‑150. (In Russ.)
https://doi.org/10.17116/oftalma2023139061144

Подписка 2026 Вестник офтальмологии (Russian Annals of Ophthalmology)
МСФ на ЯМ
Использование инфографики авторами научных работ
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Abstract:

Parry-Romberg syndrome (PRS) is a rare degenerative disease of unknown etiology, characterized by slow progressive hemifacial atrophy of the soft tissues (subcutaneous fat, muscles), cartilage and bones. Beside hemifacial atrophy, various ophthalmic and periocular manifestations of PRS has been described. Progressive enophthalmos and eyelid changes are only some of many other symptoms, as the disease can affect all layers of the eyeball. This article reviews literature on ophthalmic manifestations of PRS and reports our own case and treatment approach for a patient with this pathology.

Keywords:

hemifacial atrophy
Parry—Romberg syndrome
enophthalmos
lagophthalmos

Authors:

Sheptulin V.A.

Krasnov Research Institute of Eye Diseases

Grusha Ya.O.

Krasnov Research Institute of Eye Diseases;
I.M. Sechenov First Moscow State Medical University (Sechenov University)

Received:

17.01.2023

Accepted:

04.10.2023

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References:

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