Introduction. Interest in the study of juvenile ossifying fibroma (JOF) is due to the rarity of the pathology and the lack of clinical recommendations for the treatment of patients with JOF. The purpose of the study is analyze of the clinical profiles, features and results of surgical treatment and monitoring of patients with JOF using the example of the work of the head and neck surgery department of the Dmitry Rogachev NMRC PHOI Material and methods. 11 patients with JOF: 6 (54.5%) boys and 5 (45.5%) girls aged 2 to 13 years (Me 10 years old) were treated at the Dmitry Rogachev NMRC PHOI in 2013—2019. They were examined and underwent surgical treatment. Results. The most frequent localization of the JOF was the ethmoidal labyrinth (9/11 patients; 81.82%), in most cases with spread into the orbit (7/11; 63.64%). The disease manifested itself most often by impaired nasal airflow (5/11; 45.46%) and / or exophthalmos (5/11; 45.46%). In all patients, the neoplasm was unilateral. 15 surgical interventions were performed in 11 patients with JOF. The most common surgical access was external — in 7 (63.64%) cases. Transnasal endoscopic tumor removal and combined approaches were performed in 4 (36.36%) and 2 (18.18%) cases, respectively. A neoplasm biopsy was performed in 2 of 11 (18.18%) patients. In most patients (7/11; 63.64%), the trabecular type of JOF was pathologically verified. The average follow-up was 19.1 (5—81) months. Complications after surgical treatment were observed in 3/10 (30%) patients: in 1 — early; in 2 — deferred. Relapse was observed in 2/10 (20%) patients; in 2/10 (20%) cases, according to the imaging data, the residual component of the neoplasm was recorded without reliable signs of continued growth. Conclusion. JOF is a rare benign neoplasm characterized by aggressive rapid growth and requiring radical surgical treatment. A feature of the JOF treatment is the complexity of the radical surgical removal of education due to its late manifestation and spread simultaneously to several anatomical structures. In some cases, the removal of the tumor leads to the formation of a defect in the facial skeleton, which requires the reconstructive plastic surgery. In this regard, it is advisable to carry out such operations in multidisciplinary centers, head and neck surgery departments.