Our experience in surgical treatment of bilateral pseudoangiomatous stromal hyperplasia in children with gigantomastia

Startseva O.I.

Sechenov First Moscow State Medical University

Bystrov A.V.

Russian Children's Clinical Hospital of the Pirogov Russian National Research Medical University

Gassan T.A.

Russian Children's Clinical Hospital of the Pirogov Russian National Research Medical University;
Institute of Plastic Surgery and Cosmetology

Isaev I.V.

Russian Children's Clinical Hospital of the Pirogov Russian National Research Medical University

Ivanov S.I.

Sechenov First Moscow State Medical University

Kiseleva D.I.

Institute of Plastic Surgery and Cosmetology

Our experience in surgical treatment of bilateral pseudoangiomatous stromal hyperplasia in children with gigantomastia

Authors:

Startseva O.I., Bystrov A.V., Gassan T.A., Isaev I.V., Ivanov S.I., Kiseleva D.I.

More about the authors

Journal: Plastic Surgery and Aesthetic Medicine. 2021;(3): 23‑31

DOI: 10.17116/plast.hirurgia202103123

Downloaded: 419

To cite this article:

Startseva OI, Bystrov AV, Gassan TA, Isaev IV, Ivanov SI, Kiseleva DI. Our experience in surgical treatment of bilateral pseudoangiomatous stromal hyperplasia in children with gigantomastia. Plastic Surgery and Aesthetic Medicine. 2021;(3):23‑31. (In Russ., In Engl.)
https://doi.org/10.17116/plast.hirurgia202103123

Подписка 2025-2 (Plastic Surgery and Aesthetic Medicine)

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INTRODUCTION

Breast hypertrophy is characterized by fast unilateral or bilateral diffuse enlargement of the mammary glands without association with growth of other parts of the body. Gigantomastia occurs in puberty almost in 80% of cases. Breast abnormalities in childhood and adolescence are diverse and most often caused by deviations from normal development. There are drugs for therapy of gigantomastia (testosterone, progesterone, dihydroprogesterone, dydrogesterone). However, therapy is often ineffective. Surgical standard is reduction mammoplasty, but only after breast growth stabilization.

MATERIAL AND METHODS

Two patients with aggressive juvenile gigantomastia were operated on at the Microsurgical Department No. 1 of the Russian Children’s Clinical Hospital. Specialists from the Department of Oncology, Reconstructive Plastic Surgery and Radiology were engaged. Both patients underwent reduction mammoplasty with free transplantation of the nipple-areola complex.

CONCLUSION

Gigantomastia in adolescent girls is a multidisciplinary problem involving pediatric surgeons, endocrinologists, gynecologists and plastic surgeons. Therefore, treatment of this pathology requires adequate diagnosis, searching for possible causes of disease and development of correct treatment strategy. Reduction mammoplasty with free transplantation of the nipple-areola complex is an effective treatment significantly alleviating social, psychological and physical stress in adolescents with gigantomastia.

Keywords:

gigantomastia

juvenile macromastia

mastectomy

reduction mammoplasty

free transplantation of the nipple-areola complex

Authors:

Startseva O.I.

Sechenov First Moscow State Medical University

Bystrov A.V.

Russian Children's Clinical Hospital of the Pirogov Russian National Research Medical University

Gassan T.A.

Russian Children's Clinical Hospital of the Pirogov Russian National Research Medical University;
Institute of Plastic Surgery and Cosmetology

Isaev I.V.

Russian Children's Clinical Hospital of the Pirogov Russian National Research Medical University

Ivanov S.I.

Sechenov First Moscow State Medical University

Kiseleva D.I.

Institute of Plastic Surgery and Cosmetology

Received:

21.05.2021

Accepted:

17.06.2021

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