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Khugaev G.A.

A.N. Bakulev National Medical Research Center for Cardiovascular Surgery of the Ministry of Health of Russia

Shmalts A.A.

A.N. Bakulev National Medical Research Center for Cardiovascular Surgery of the Ministry of Health of Russia;
Russian Medical Academy of Continuing Professional Education of the Ministry of Health of Russia

Morphological assessment of pulmonary vessels in pulmonary arterial hypertension associated with congenital heart disease

Authors:

Khugaev G.A., Shmalts A.A.

More about the authors

Journal: Russian Journal of Archive of Pathology. 2021;83(5): 49‑57

DOI: 10.17116/patol20218305149

Read: 7492 times

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MORPHOLOGICAL ASSESSMENT OF PULMONARY VESSELS IN PULMONARY ARTERIAL HYPERTENSION ASSOCIATED WITH CONGENITAL HEART DISEASE
MORPHOLOGICAL ASSESSMENT OF PULMONARY VESSELS IN PULMONARY ARTERIAL HYPERTENSION ASSOCIATED WITH CONGENITAL HEART DISEASE

To cite this article:

Khugaev GA, Shmalts AA. Morphological assessment of pulmonary vessels in pulmonary arterial hypertension associated with congenital heart disease. Russian Journal of Archive of Pathology. 2021;83(5):49‑57. (In Russ.)
https://doi.org/10.17116/patol20218305149

Подписка 2026 Архив патологии (Russian Journal of Archive of Pathology)
МСФ на ЯМ
Использование инфографики авторами научных работ
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Abstract:

Pulmonary vascular remodeling is the key structural alteration in pulmonary arterial hypertension associated with congenital heart disease (CHD). Changes in the pulmonary vessels in CHD generally occur in the inner and middle coats. This review considers the pathology of these changes and highlights some issues of a stereological approach to the morphometry of pulmonary vasculature. It also touches upon the issues of the morphology of pulmonary vessels in post-capillary and segmental pulmonary hypertension.

Keywords:

pulmonary arterial hypertension
congenital heart disease
pulmonary vessels
remodeling
stereology

Authors:

Khugaev G.A.

A.N. Bakulev National Medical Research Center for Cardiovascular Surgery of the Ministry of Health of Russia

Shmalts A.A.

A.N. Bakulev National Medical Research Center for Cardiovascular Surgery of the Ministry of Health of Russia;
Russian Medical Academy of Continuing Professional Education of the Ministry of Health of Russia

Received:

15.04.2021

Accepted:

28.06.2021

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