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Anikin I.A.

St. Petersburg Research Institute of Ear, Throat, Nose and Speech

Khamgushkeeva N.N.

St. Petersburg Research Institute of Ear, Throat, Nose and Speech

Knyazev A.D.

St. Petersburg Research Institute of Ear, Throat, Nose and Speech

Mamedova A.D.

St. Petersburg Research Institute of Ear, Throat, Nose and Speech

Congenital cholesteatoma of the middle ear with total atresia of the external auditory canal: two cases report

Authors:

Anikin I.A., Khamgushkeeva N.N., Knyazev A.D., Mamedova A.D.

More about the authors

Journal: Russian Bulletin of Otorhinolaryngology. 2025;90(3): 73‑78

DOI: 10.17116/otorino20259003173

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Table of contents

CONGENITAL CHOLESTEATOMA OF THE MIDDLE EAR WITH TOTAL ATRESIA OF THE EXTERNAL AUDITORY CANAL: TWO CASES REPORT
CONGENITAL CHOLESTEATOMA OF THE MIDDLE EAR WITH TOTAL ATRESIA OF THE EXTERNAL AUDITORY CANAL: TWO CASES REPORT

To cite this article:

Anikin IA, Khamgushkeeva NN, Knyazev AD, Mamedova AD. Congenital cholesteatoma of the middle ear with total atresia of the external auditory canal: two cases report. Russian Bulletin of Otorhinolaryngology. 2025;90(3):73‑78. (In Russ.)
https://doi.org/10.17116/otorino20259003173

Подписка 2026 Вестник оториноларингологии (Russian Bulletin of Otorhinolaryngology)
 
МСФ на ЯМ
Использование инфографики авторами научных работ
Abstract:

Congenital stenosis and atresia of the external auditory canal are the most common developmental anomalies of the external ear. Cases of combination of these malformations with cholesteatoma of the temporal bone have been repeatedly described in the world literature. This combined pathology is more typical of congenital stenosis of the external auditory canal. Total atresia of the external auditory canal is rarely associated with cholesteatoma. Cholesteatoma found behind the atretic plate is classified as congenital, excluding other possible mechanisms of it’s formation. The article presents two clinical cases of a combination of congenital cholesteatoma and complete atresia of the external auditory canal: in an 8-year old girl and a 19-year old boy without the development of intratemporal and extratemporal complications.

Keywords:

congenital cholesteatoma
middle ear
total atresia of the external auditory canal
complete atresia of the external auditory canal
complete aural atresia

Authors:

Anikin I.A.

St. Petersburg Research Institute of Ear, Throat, Nose and Speech

Khamgushkeeva N.N.

St. Petersburg Research Institute of Ear, Throat, Nose and Speech

Knyazev A.D.

St. Petersburg Research Institute of Ear, Throat, Nose and Speech

Mamedova A.D.

St. Petersburg Research Institute of Ear, Throat, Nose and Speech

Received:

08.06.2024

Accepted:

24.07.2024

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