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Iukina M.Iu.

FGU Éndokrinologicheskiĭ nauchnyĭ tsentr, Moskva

Tiul'pakov A.N.

Éndokrinologicheskiĭ nauchnyĭ tsentr, Moskva

Troshina E.A.

Éndokrinologicheskiĭ nauchnyĭ tsentr, Moskva

Bel'tsevich D.G.

Éndokrinologicheskiĭ nauchnyĭ tsentr, Moskva

Von Hippel-Lindau disease (VHL-syndrome)

Authors:

Iukina M.Iu., Tiul'pakov A.N., Troshina E.A., Bel'tsevich D.G.

More about the authors

Journal: Problems of Endocrinology. 2012;58(2): 34‑41

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VON HIPPEL-LINDAU DISEASE (VHL-SYNDROME)
VON HIPPEL-LINDAU DISEASE (VHL-SYNDROME)

To cite this article:

Iukina MIu, Tiul'pakov AN, Troshina EA, Bel'tsevich DG. Von Hippel-Lindau disease (VHL-syndrome). Problems of Endocrinology. 2012;58(2):34‑41. (In Russ.)

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Von Hippel-Lindau disease is a hereditary tumour syndrome associated with the earlier development of a variety of benign and malignant neoplasms, such as hemangioblastomas of the central nervous system and retina, tumours of the internal ear, renal carcinoma and cysts, pheochromocytoma, neuroendocrine tumours, pancreatic cysts, epididymal and broad ligament cystadenomas in men and women respectively. Von Hippel-Lindau disease is considered to be the most common cause of hereditary renal cancer.

Keywords:

Von Hippel-Lindau disease
pheochromocytoma
hemangioblastoma
tumour

Authors:

Iukina M.Iu.

FGU Éndokrinologicheskiĭ nauchnyĭ tsentr, Moskva

Tiul'pakov A.N.

Éndokrinologicheskiĭ nauchnyĭ tsentr, Moskva

Troshina E.A.

Éndokrinologicheskiĭ nauchnyĭ tsentr, Moskva

Bel'tsevich D.G.

Éndokrinologicheskiĭ nauchnyĭ tsentr, Moskva

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