Dysfunction of the right ventricular outflow tract and pulmonary artery is often found in patients with congenital heart defects. In most cases, open surgery is often associated with high risk due to repeated pulmonary valve replacement throughout the life. Transcatheter pulmonary valve replacement is one of the most progressive achievements in the treatment of pulmonary artery dysfunction. This approach has become a clear alternative to surgical intervention in these patients. In this review, we analyzed pathophysiology of pulmonary valve dysfunction on example of tetralogy of Fallot, indications for transcatheter pulmonary valve implantation, results and possible complications. Aspects of clinical application and valve technology are also highlighted. To date, transcatheter pulmonary valve implantation is actively used as an alternative to surgical intervention for dysfunction of pulmonary valve and right ventricular outflow tract. Nevertheless, the number of patients with complex morphology of right ventricular outflow and pulmonary artery who cannot undergo percutaneous valve implantation is significant.