Arteriovenous malformation (AVM, arteriovenous dysplasia) is one of the variants of congenital vascular defects formed as a result of a defect in the development of the arterial and venous systems during ontogenesis with the formation of direct messages between vessels of different diameters. In this regard, high-speed shunting of blood from the arterial part of the vascular system to the venous through fistulas of various calibers occurs. This disease is characterized by a variety of clinical manifestations. The auricle is the second most common site of extracranial AVM. Despite a large number of studies concerning etiological factors, diagnostic criteria and clinical aspects, differential diagnosis of auricular AVM in some cases is still difficult. The experience of differential diagnosis and sequence of actions in case of suspected auricular AVM is presented on the example of a clinical case.