Diffuse choroidal hemangioma as a manifestation of Sturge—Weber syndrome (a clinical case study)

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Stoiukhina A.S.

FGBU "NII glaznykh bolezneĭ" RAMN, Moskva

Ismailova D.S.

FGBU "NII glaznykh bolezneĭ" RAMN, Moskva;
GBOU VPO "Pervyĭ Moskovskiĭ gosudarstvennyĭ meditsinskiĭ universitet im. I.M. Sechenova" Minzdrava RF

Diffuse choroidal hemangioma as a manifestation of Sturge—Weber syndrome (a clinical case study)

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Stoiukhina A.S., Ismailova D.S.

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Journal: Russian Annals of Ophthalmology. 2019;135(6): 108‑116

DOI: 10.17116/oftalma2019135061108

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To cite this article:

Stoiukhina AS, Ismailova DS. Diffuse choroidal hemangioma as a manifestation of Sturge—Weber syndrome (a clinical case study). Russian Annals of Ophthalmology. 2019;135(6):108‑116. (In Russ.)
https://doi.org/10.17116/oftalma2019135061108

Подписка 2025 (Russian Annals of Ophthalmology)

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Encephalotrigeminal angiomatosis (Sturge—Weber syndrome) is a congenital sporadic disease characterized by angiomatosis of meningeal vessels, facial and eye capillaries. The article presents a clinical case of comorbidity between monolateral skin angioma, ipsilateral conjunctival and choroidal angiomas without intraocular pressure elevation. The case is unusual due to asynchronous manifestation of the clinical signs of Sturge—Weber syndrome. Facial angioma was diagnosed at birth, while conjunctival angioma appeared at the age of 45 — at the same time as monolateral hypermetropia, which may be the first symptom of diffuse choroidal angioma.

Keywords:

diffuse choroidal hemangioma

Sturge—Weber syndrome

Authors:

Stoiukhina A.S.

FGBU "NII glaznykh bolezneĭ" RAMN, Moskva

Ismailova D.S.

FGBU "NII glaznykh bolezneĭ" RAMN, Moskva;
GBOU VPO "Pervyĭ Moskovskiĭ gosudarstvennyĭ meditsinskiĭ universitet im. I.M. Sechenova" Minzdrava RF

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