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Iukina M.Iu.

FGU Éndokrinologicheskiĭ nauchnyĭ tsentr, Moskva

Goncharov N.P.

FGU Éndokrinologicheskiĭ nauchnyĭ tsentr, Moskva

Bel'tsevich D.G.

Éndokrinologicheskiĭ nauchnyĭ tsentr, Moskva

Troshina E.A.

Éndokrinologicheskiĭ nauchnyĭ tsentr, Moskva

Multiple type 2 endocrine neoplasia (case report)

Authors:

Iukina M.Iu., Goncharov N.P., Bel'tsevich D.G., Troshina E.A.

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Journal: Problems of Endocrinology. 2011;57(6): 21‑26

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MULTIPLE TYPE 2 ENDOCRINE NEOPLASIA (CASE REPORT)
MULTIPLE TYPE 2 ENDOCRINE NEOPLASIA (CASE REPORT)

To cite this article:

Iukina MIu, Goncharov NP, Bel'tsevich DG, Troshina EA. Multiple type 2 endocrine neoplasia (case report). Problems of Endocrinology. 2011;57(6):21‑26. (In Russ.)

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Recommended articles:
Difficulties of diagnosing a clinically silent pheochromocytoma. Russian Journal of Preventive Medi­cine. 2025;(3):107-111

The congenital form of pheochromocytoma is known to be fraught with high risk of post-treatment relapse, bilateral, multicentric or primarily multiple lesions. The patients presenting with the syndrome of multiple type 2 endocrine neoplasia usually have no extra-adrenal pheochromocytomas or metastases. Both examination and treatment of these patients should be performed taking these peculiarities into consideration. We describe a family with multiple type 2 endocrine neoplasia and highlight selected aspects of the management of the patients presenting with genetically determined pheochromocytoma.

Keywords:

multiple type 2 endocrine neoplasia
pheochromocytoma
RET gene mutation
medullary thyroid cancer
multiple type 2 endocrine neoplasia
pheochromocytoma
RET gene mutation
medullary thyroid cancer

Authors:

Iukina M.Iu.

FGU Éndokrinologicheskiĭ nauchnyĭ tsentr, Moskva

Goncharov N.P.

FGU Éndokrinologicheskiĭ nauchnyĭ tsentr, Moskva

Bel'tsevich D.G.

Éndokrinologicheskiĭ nauchnyĭ tsentr, Moskva

Troshina E.A.

Éndokrinologicheskiĭ nauchnyĭ tsentr, Moskva

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