Sex cord tumor with annular tubules

Badlaeva A.S.; Tregubova A.V.; Matronitskii R.B.; Raksha A.P.; Sukhoparova V.V.; Lysova N.L.; Asaturova A.V.

doi:https://doi.org/10.17116/patol20258701148

Badlaeva A.S.

National Medical Research Center for Obstetrics, Gynecology and Perinatology named after Academician V.I. Kulakov

ORCID: 0000-0001-5223-9767

Tregubova A.V.

National Medical Research Center for Obstetrics, Gynecology and Perinatology named after Academician V.I. Kulakov

ORCID: 0000-0003-4601-1330

Matronitskii R.B.

National Medical Research Center for Obstetrics, Gynecology and Perinatology named after Academician V.I. Kulakov

ORCID: 0000-0002-4145-5947

Raksha A.P.

N.I. Pirogov Russian National Research Medical University

ORCID: 0009-0003-5193-9413

Sukhoparova V.V.

N.I. Pirogov Russian National Research Medical University

ORCID: 0000-0002-9358-0483

Lysova N.L.

N.I. Pirogov Russian National Research Medical University

ORCID: 0009-0000-5762-391X

Asaturova A.V.

National Medical Research Center for Obstetrics, Gynecology and Perinatology named after academician V.I. Kulakov

ORCID: 0000-0001-8739-5209

Sex cord tumor with annular tubules

Authors:

Badlaeva A.S., Tregubova A.V., Matronitskii R.B., Raksha A.P., Sukhoparova V.V., Lysova N.L., Asaturova A.V.

More about the authors

Journal: Russian Journal of Archive of Pathology. 2025;87(1): 48‑52

DOI: 10.17116/patol20258701148

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To cite this article:

Badlaeva AS, Tregubova AV, Matronitskii RB, Raksha AP, Sukhoparova VV, Lysova NL, Asaturova AV. Sex cord tumor with annular tubules. Russian Journal of Archive of Pathology. 2025;87(1):48‑52. (In Russ.)
https://doi.org/10.17116/patol20258701148

Подписка 2026 Архив патологии (Russian Journal of Archive of Pathology)

Использование инфографики авторами научных работ

Abstract:

Sex cord tumor with annular tubules is a rare type of ovarian tumor, which seems to arise from Sertoli cells. Most tumors are associated with Peutz—Jeghers syndrome and have a benign course and favorable prognosis; however, about 20% of sporadic sex cord tumors with annular tubules have a high risk of developing metastases. We present a case report about 18-year-old patient who presented with irregular menstruation and abdominal pain. Based on the histological features and immunohistochemical results, the diagnosis of a sex cord tumor with annular tubules was confirmed. The above-described ovarian tumor is rare in childhood and adolescence compared to the general population, which, combined with nonspecific clinical manifestations, can result certain diagnostic difficulties in this age group of patients.

Keywords:

sex cord tumor with annular tubules

sex cord stromal tumors

Peutz—Jeghers syndrome

Authors:

Badlaeva A.S.

National Medical Research Center for Obstetrics, Gynecology and Perinatology named after Academician V.I. Kulakov

ORCID: 0000-0001-5223-9767

Tregubova A.V.

National Medical Research Center for Obstetrics, Gynecology and Perinatology named after Academician V.I. Kulakov

ORCID: 0000-0003-4601-1330

Matronitskii R.B.

National Medical Research Center for Obstetrics, Gynecology and Perinatology named after Academician V.I. Kulakov

ORCID: 0000-0002-4145-5947

Raksha A.P.

N.I. Pirogov Russian National Research Medical University

ORCID: 0009-0003-5193-9413

Sukhoparova V.V.

N.I. Pirogov Russian National Research Medical University

ORCID: 0000-0002-9358-0483

Lysova N.L.

N.I. Pirogov Russian National Research Medical University

ORCID: 0009-0000-5762-391X

Asaturova A.V.

National Medical Research Center for Obstetrics, Gynecology and Perinatology named after academician V.I. Kulakov

ORCID: 0000-0001-8739-5209

Received:

28.09.2024

Accepted:

30.10.2024

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References:

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