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Sidorov I.V.

Dmitry Rogachev National Medical Research Center of Pediatric Hematology, Oncology and Immunology

Fedorova A.S.

Lomonosov Moscow State University

Konopleva E.I.

Dmitry Rogachev National Medical Research Center of Pediatric Hematology, Oncology and Immunology

Makarova N.P.

Dmitry Rogachev National Medical Research Center of Pediatric Hematology, Oncology and Immunology

Sharlai A.S.

Dmitry Rogachev National Medical Research Center of Pediatric Hematology, Oncology and Immunology

Konovalov D.M.

Dmitry Rogachev National Medical Research Center of Pediatric Hematology, Oncology and Immunology;
Russian Medical Academy of Continuous Professional Education

CIC-rearranged sarcoma: a case report and literature review

Authors:

Sidorov I.V., Fedorova A.S., Konopleva E.I., Makarova N.P., Sharlai A.S., Konovalov D.M.

More about the authors

Journal: Russian Journal of Archive of Pathology. 2023;85(3): 64‑70

DOI: 10.17116/patol20238503164

Read: 3280 times

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Table of contents

CIC-REARRANGED SARCOMA: A CASE REPORT AND LITERATURE REVIEW
CIC-REARRANGED SARCOMA: A CASE REPORT AND LITERATURE REVIEW

To cite this article:

Sidorov IV, Fedorova AS, Konopleva EI, Makarova NP, Sharlai AS, Konovalov DM. CIC-rearranged sarcoma: a case report and literature review. Russian Journal of Archive of Pathology. 2023;85(3):64‑70. (In Russ.)
https://doi.org/10.17116/patol20238503164

Подписка 2026 Архив патологии (Russian Journal of Archive of Pathology)
МСФ на ЯМ
Использование инфографики авторами научных работ
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Abstract:

CIC-rearranged sarcoma is a rare and extremely aggressive tumor that occurs mainly in soft tissues. Despite the fact that identification of a characteristic genetic rearrangement is necessary to verify the diagnosis, in most cases, the correct diagnosis can be made by comparing histological signs and a characteristic immunophenotype, which greatly speeds up the diagnosis. The article describes a case of CIC-rearranged sarcoma in a 14-year girl with the successful application of the CWS-2009 treatment protocol.

Keywords:

CIC-rearranged sarcoma
Ewing-like sarcomas
undifferentiated small round cell sarcoma

Authors:

Sidorov I.V.

Dmitry Rogachev National Medical Research Center of Pediatric Hematology, Oncology and Immunology

Fedorova A.S.

Lomonosov Moscow State University

Konopleva E.I.

Dmitry Rogachev National Medical Research Center of Pediatric Hematology, Oncology and Immunology

Makarova N.P.

Dmitry Rogachev National Medical Research Center of Pediatric Hematology, Oncology and Immunology

Sharlai A.S.

Dmitry Rogachev National Medical Research Center of Pediatric Hematology, Oncology and Immunology

Konovalov D.M.

Dmitry Rogachev National Medical Research Center of Pediatric Hematology, Oncology and Immunology;
Russian Medical Academy of Continuous Professional Education

Received:

13.12.2022

Accepted:

22.02.2023

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References:

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