Treatment of malignant peripheral nerve sheath tumors: case reports and a literature review

Konovalov N.A.

OOO Klinika spinal'noĭ neĭrokhirurgii «Aksis»;
NII neĭrokhirurgii im. akad. N.N. Burdenko RAMN, Moskva

ORCID: 0000-0003-0824-1848

Korolishin V.A.

OOO Klinika spinal'noĭ neĭrokhirurgii «Aksis»;
NII neĭrokhirurgii im. akad. N.N. Burdenko RAMN, Moskva

Asiutin D.S.

FGBU "NII neĭrokhirurgii im. akad. N.N. Burdenko" RAMN, Moskva

Timonin S.Iu.

Pervyĭ MGMU im. I.M. Sechenova, Moskva

Shults M.A.

Burdenko Neurosurgical Center, Moscow, Russia

Solenkova A.V.

Burdenko Neurosurgical Institute, Moscow, Russia

Zakirov B.A.

FGBNU "NII neĭrokhirurgii im. akad. N.N. Burdenko", RAMN, Moskva

Batyrov A.A.

Burdenko Neurosurgical Institute, Moscow, Russia

Treatment of malignant peripheral nerve sheath tumors: case reports and a literature review

Authors:

Konovalov N.A., Korolishin V.A., Asiutin D.S., Timonin S.Iu., Shults M.A., Solenkova A.V., Zakirov B.A., Batyrov A.A.

More about the authors

Journal: Burdenko's Journal of Neurosurgery. 2019;83(3): 64‑72

DOI: 10.17116/neiro20198303164

Downloaded: 302

To cite this article:

Konovalov NA, Korolishin VA, Asiutin DS, et al. . Treatment of malignant peripheral nerve sheath tumors: case reports and a literature review. Burdenko's Journal of Neurosurgery. 2019;83(3):64‑72. (In Russ., In Engl.)
https://doi.org/10.17116/neiro20198303164

Подписка 2025-2 (Burdenko's Journal of Neurosurgery)

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Malignant peripheral nerve sheath tumors (MPNSTs) are soft tissue sarcomas that develop from peripheral nerve sheath cells (T. Hirose, B.W. Scheithauer). These tumors are characterized by aggressive growth with an unfavorable outcome and may develop de novo or through malignant transformation of schwannomas, neurofibromas, or ganglioneuromas. MPNSTs are characterized by a rapid course and a poor prognosis. In this article, we reported cases of patients with malignant peripheral nerve tumors of the brachial plexus trunks and spinal localization.

Keywords:

malignant neurofibroma

neurogenic sarcoma

malignant peripheral nerve sheath tumor

Authors:

Konovalov N.A.

OOO Klinika spinal'noĭ neĭrokhirurgii «Aksis»;
NII neĭrokhirurgii im. akad. N.N. Burdenko RAMN, Moskva

ORCID: 0000-0003-0824-1848

Korolishin V.A.

OOO Klinika spinal'noĭ neĭrokhirurgii «Aksis»;
NII neĭrokhirurgii im. akad. N.N. Burdenko RAMN, Moskva

Asiutin D.S.

FGBU "NII neĭrokhirurgii im. akad. N.N. Burdenko" RAMN, Moskva

Timonin S.Iu.

Pervyĭ MGMU im. I.M. Sechenova, Moskva

Shults M.A.

Burdenko Neurosurgical Center, Moscow, Russia

Solenkova A.V.

Burdenko Neurosurgical Institute, Moscow, Russia

Zakirov B.A.

FGBNU "NII neĭrokhirurgii im. akad. N.N. Burdenko", RAMN, Moskva

Batyrov A.A.

Burdenko Neurosurgical Institute, Moscow, Russia

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