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Asmanov A.I.

N.I. Pirogov Russian National Research Medical University, Ministry of Health of the Russian Federation, Moscow, Russia, 117997;
Academician Yu.E. Veltishchev Research Clinical Institute of Pediatrics of the N.I. Pirogov Russian National Research Medical University, Ministry of Health of the Russian Federation, Moscow, Russia, 125412

Zlobina N.V.

Kafedra otorinolaringologii pediatricheskogo fakul'teta RNIMU im. N.I. Pirogova Minzdrava Rossii Moskva, Rossiia, 117997

Radtsig E.Iu.

Kafedra otorinolaringologii pediatricheskogo fakul'teta RNIMU im. N.I. Pirogova, Moskva

Polev G.A.

Dmitry Rogachev National Research Center of Pediatric Hematology, Oncology, and Immunology, Moscow, Russia

Sorokina E.V.

GOU VPO MGUPP NIUV, Moskva

Polypous pansinusitis with the deformation of the external nose in a 8 year-old child presenting with the primary ciliary dyskinesia syndrome

Authors:

Asmanov A.I., Zlobina N.V., Radtsig E.Iu., Polev G.A., Sorokina E.V.

More about the authors

Journal: Russian Bulletin of Otorhinolaryngology. 2017;82(5): 61‑63

DOI: 10.17116/otorino201782561-63

Views: 2413

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To cite this article:

Asmanov AI, Zlobina NV, Radtsig EIu, Polev GA, Sorokina EV. Polypous pansinusitis with the deformation of the external nose in a 8 year-old child presenting with the primary ciliary dyskinesia syndrome. Russian Bulletin of Otorhinolaryngology. 2017;82(5):61‑63. (In Russ.)
https://doi.org/10.17116/otorino201782561-63

Подписка 2025 (Russian Bulletin of Otorhinolaryngology)
 
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This article reports a rare observation of the development of chronic polypous pansinusitis with deformation of the external nose in a 8 year-old child presenting with primary ciliary dyskinesia syndrome. The patient underwent multiple surgical interventions in the preceding period. The key argument in favour of the definitive diagnosis was the results of investigation of ciliated epithelium biopsy taken from the nasal cavity and bronchi in combination with the data obtained by diagnostic endoscopy of the nasal cavity and nasopharynx supplemented by computed tomography. The proposed treatment strategy including endoscopic endonasal pansinusotomy, antibacterial therapy taking into consideration the sensitivity of the seeded microorganism, and hormonal therapy proved optimal for the management of the given patient.

Keywords:

childhood
chronic polypous pansinusitis
ciliary dyskinesia syndrome
endoscopy
adenotomy
polypotomy
endonasal surgery

Authors:

Asmanov A.I.

N.I. Pirogov Russian National Research Medical University, Ministry of Health of the Russian Federation, Moscow, Russia, 117997;
Academician Yu.E. Veltishchev Research Clinical Institute of Pediatrics of the N.I. Pirogov Russian National Research Medical University, Ministry of Health of the Russian Federation, Moscow, Russia, 125412

Zlobina N.V.

Kafedra otorinolaringologii pediatricheskogo fakul'teta RNIMU im. N.I. Pirogova Minzdrava Rossii Moskva, Rossiia, 117997

Radtsig E.Iu.

Kafedra otorinolaringologii pediatricheskogo fakul'teta RNIMU im. N.I. Pirogova, Moskva

Polev G.A.

Dmitry Rogachev National Research Center of Pediatric Hematology, Oncology, and Immunology, Moscow, Russia

Sorokina E.V.

GOU VPO MGUPP NIUV, Moskva

List of references:

  1. Takeuchi K, Kitano M, Ishinaga H, Kobayashi M, Ogawa S, Nakatani K, Masuda S, Nagao M, Fujisawa T. Recent advances in primary ciliary dyskinesia. Auris Nasus Larynx. 2016;43(3):229-236. https://doi.org/10.1016/j.anl.2015.09.012
  2. Rozinova NN, Mizernitskii YuL. Orfannye zabolevaniya legkikh u detei. M.: Medpraktika-M; 2015. (In Russ.)
  3. Stenner M, Rudack C. Diseases of the nose and paranasal sinuses in childhood. Laryngorhinootologie. 2014;93(suppl 1):24-48. https://doi.org/10.1055/s-0033-1363211
  4. Fitzgerald DA, Shapiro AJ. When to suspect primary ciliary dyskinesia in children. Paediatr Respir Rev. 2016;18:3-7. https://doi.org/10.1016/j.prrv.2015.11.006
  5. Barbato A, Frischer T, Kuehni CE, et al. Primary ciliary dyskinesia: a consensus statement on diagnostic and treatment approaches in children. Eur Respir J. 2009;34:1264-1276.
  6. Kurkowiak M, Ziętkiewicz E, Witt M. Recent advances in primary ciliary dyskinesia genetics. J Med Genet. 2015;52(1):1-9. https://doi.org/10.1136/jmedgenet-2014-102755
  7. Mata M, Milian L, Armengot M, Carda C. Gene mutations in primary ciliary dyskinesia related to otitis media. Curr Allergy Asthma Rep. 2014;14(3):420. https://doi.org/10.1007/s11882-014-0420-1
  8. Jankowski R, Pigret D, Decroocq F, Blum A, Gillet P. Comparison of radical (nasalisation) and functional ethmoidectomy in patients with severe sinonasal polyposis. A retrospective study. Rev Laryngol Otol Rhinol (Bord). 2006;127(3):131-140.

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