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Zainulabidov R.A.

Children’s City Clinical Hospital named after N.F. Filatov

Razumovsky A.Yu.

Children’s City Clinical Hospital named after N.F. Filatov;
Pirogov Russian National Research Medical University

Mitupov Z.B.

Children’s City Clinical Hospital named after N.F. Filatov;
Pirogov Russian National Research Medical University

Chumakova G.Yu.

Children’s City Clinical Hospital named after N.F. Filatov

Teplov V.O.

Children’s City Clinical Hospital named after N.F. Filatov

Titova E.A.

Children’s City Clinical Hospital named after N.F. Filatov

Zolotareva L.S.

N.F. Filatov Children’s City Clinical Hospital;
Pirogov Russian National Research Medical University

Surgical treatment of children with celiac axis compression syndrome

Authors:

Zainulabidov R.A., Razumovsky A.Yu., Mitupov Z.B., Chumakova G.Yu., Teplov V.O., Titova E.A., Zolotareva L.S.

More about the authors

Journal: Pirogov Russian Journal of Surgery. 2025;(6): 58‑68

DOI: 10.17116/hirurgia202506158

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Table of contents

SURGICAL TREATMENT OF CHILDREN WITH CELIAC AXIS COMPRESSION SYNDROME
SURGICAL TREATMENT OF CHILDREN WITH CELIAC AXIS COMPRESSION SYNDROME

To cite this article:

Zainulabidov RA, Razumovsky AYu, Mitupov ZB, Chumakova GYu, Teplov VO, Titova EA, Zolotareva LS. Surgical treatment of children with celiac axis compression syndrome. Pirogov Russian Journal of Surgery. 2025;(6):58‑68. (In Russ.)
https://doi.org/10.17116/hirurgia202506158

Подписка 2026 Хирургия. Журнал им. Н.И. Пирогова (Pirogov Russian Journal of Surgery)
МСФ на ЯМ
Использование инфографики авторами научных работ
Recommended articles:
Simu­ltaneous surgeries for celiac axis compression syndrome (Dunbar syndrome) in children. Piro­gov Russian Journal of Surgery. 2025;(10):80-87
Abstract:

OBJECTIVE

To establish the indications for surgical treatment of celiac axis compression syndrome (CACS) in childhood, efficacy of laparoscopic decompression in these patients, possible complications and risks of surgical treatment.

MATERIAL AND METHODS

A total of 148 patients aged 4—17 years underwent surgical treatment for CACS between 2015 and 2023. Of these, 92 patients were followed-up in long-term postoperative period. The leading clinical manifestation was abdominal pain. The diagnosis was based on anamnesis, physical examination, Doppler ultrasound of celiac axis with blood flow velocity measurement, endoscopic ultrasonography and angiography. After examination, all patients underwent celiac axis decompression. According to intraoperative data, the main cause of celiac axis compression was the median arcuate ligament combined with neurofibrous tissue of celiac plexus.

RESULTS

Mean surgery time was 55 min. Intraoperative blood loss did not exceed 5—30 ml. There were 2 conversions. Patients were discharged. Postoperative examination was performed in 3—36 months after full recovery.

CONCLUSION

The authors identified the indications for surgical treatment of CACS, estimated clinical status of patients in pre- and postoperative period, proposed the diagnostic and treatment algorithm, as well as described the benefits of laparoscopic celiac axis decompression in children. Our experience demonstrates the possibility of early diagnosis of CACS and successful laparoscopic treatment.

Keywords:

Celiac axis compression syndrome
Dunbar syndrome
surgical treatment of celiac axis compression syndrome
laparoscopic decompression of celiac axis

Authors:

Zainulabidov R.A.

Children’s City Clinical Hospital named after N.F. Filatov

Razumovsky A.Yu.

Children’s City Clinical Hospital named after N.F. Filatov;
Pirogov Russian National Research Medical University

Mitupov Z.B.

Children’s City Clinical Hospital named after N.F. Filatov;
Pirogov Russian National Research Medical University

Chumakova G.Yu.

Children’s City Clinical Hospital named after N.F. Filatov

Teplov V.O.

Children’s City Clinical Hospital named after N.F. Filatov

Titova E.A.

Children’s City Clinical Hospital named after N.F. Filatov

Zolotareva L.S.

N.F. Filatov Children’s City Clinical Hospital;
Pirogov Russian National Research Medical University

Received:

03.08.2024

Accepted:

26.09.2024

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