IgG4-related chronic periaortitis with retroperitoneal fibrosis

Pal'tseva E.M.; Dolzhansky O.V.; Morozova M.M.; Lishchuk S.V.; Stepanenko A.B.; Charchian É.R.; Fedorov D.N.

doi:https://doi.org/

Pal'tseva E.M.

Laboratoriia élektronnoĭ mikroskopii i immunogistokhimii Tsentralizovannogo patologoanatomicheskogo otdeleniia GBOU VPO "Pervyĭ Moskovskiĭ gosudarstvennyĭ meditsinskiĭ universitet im. I.M. Sechenova" Minzdravsotsrazvitiia Rossii

Dolzhansky O.V.

Petrovsky Russian Research Center for Surgery, Moscow, Russia

Morozova M.M.

Otdelenie khirurgii porokov serdtsa Rossiĭskogo nauchnogo tsentra khirurgii im. akad. B.V. Petrovskogo RAMN, Moskva

Lishchuk S.V.

GU "Moskovskiĭ oblastnoĭ nauchno-issledovatel'skiĭ klinicheskiĭ institut im. M.F. Vladimirskogo"

Stepanenko A.B.

RNTsKh im. akad. B.V. Petrovskogo RAMN, Moskva

SPIN RSCI: 7602-1603
Scopus AuthorID: 7005363160
ORCID: 0000-0002-8768-127X

Charchian É.R.

RNTsKh im. akad. B.V. Petrovskogo RAMN

SPIN RSCI: 4641-0523
Scopus AuthorID: 14044681400
ORCID: 0000-0002-0488-2560

Fedorov D.N.

RNTsKh im. akad. B.V. Petrovskogo RAMN, Moskva

IgG4-related chronic periaortitis with retroperitoneal fibrosis

Authors:

Pal'tseva E.M., Dolzhansky O.V., Morozova M.M., Lishchuk S.V., Stepanenko A.B., Charchian É.R., Fedorov D.N.

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Journal: Russian Journal of Archive of Pathology. 2014;76(2): 32‑35

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To cite this article:

Pal'tseva EM, Dolzhansky OV, Morozova MM, Lishchuk SV, Stepanenko AB, Charchian ÉR, Fedorov DN. IgG4-related chronic periaortitis with retroperitoneal fibrosis. Russian Journal of Archive of Pathology. 2014;76(2):32‑35. (In Russ.)

Подписка 2026 Архив патологии (Russian Journal of Archive of Pathology)

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Abstract:

The paper describes a case of IgG4-related chronic periaortitis in a 56-year-old man. Computed tomography revealed stenosis of the abdominal aorta and both common iliac arteries due to calcified atherosclerotic plaques, in this connection, bifurcation aorta-common femoral bypass surgery was performed. Intraoperatively, a solid retroperitoneal mass intimately connected with the walls of vessels was revealed in the retroperitoneal space around the aorta and iliac arteries. Histological examination ascertained rough fibrous connective tissue growth, a marked lymphoplasmacytic infiltration with an admixture of eosinophils, and formation of lymphoid follicles with germinal centers. Immunohistochemical examination revealed the plasma cell expression of CD20, IgG, IgG4, and kappa and lambda light chains in the inflammatory infiltrate. Because of active immune inflammation, further conservative therapy was recommended.

Keywords:

IgG4-related disease

IgG4-related chronic periaortitis

IgG4

Authors:

Pal'tseva E.M.

Dolzhansky O.V.

Petrovsky Russian Research Center for Surgery, Moscow, Russia

Morozova M.M.

Otdelenie khirurgii porokov serdtsa Rossiĭskogo nauchnogo tsentra khirurgii im. akad. B.V. Petrovskogo RAMN, Moskva

Lishchuk S.V.

GU "Moskovskiĭ oblastnoĭ nauchno-issledovatel'skiĭ klinicheskiĭ institut im. M.F. Vladimirskogo"

Stepanenko A.B.

RNTsKh im. akad. B.V. Petrovskogo RAMN, Moskva

SPIN RSCI: 7602-1603
Scopus AuthorID: 7005363160
ORCID: 0000-0002-8768-127X

Charchian É.R.

RNTsKh im. akad. B.V. Petrovskogo RAMN

SPIN RSCI: 4641-0523
Scopus AuthorID: 14044681400
ORCID: 0000-0002-0488-2560

Fedorov D.N.

RNTsKh im. akad. B.V. Petrovskogo RAMN, Moskva

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References:

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